“Ebstein's anomaly is a rare cardiac anomaly that occurs in approximately one in 20,000 live births and accounts for less than 1% of all congenital heart disease (Ebstein anomaly in adults). The purpose of this article is to review Ebstein's anomaly - to understand what it is, how it affects the heart, possible symptoms and other possible complications associated with this anomaly. The diagnosis of this abnormality is essential in the treatment of patients, which is why echocardiography along with other testing modalities are essential to evaluate the available treatment options, as well as to discern what the prognosis may be. Advanced testing modalities have made it possible to distinguish Ebstein's anomaly from other differential diagnoses. Developments in testing modalities coupled with comprehensive calculations, formulas and measurements have facilitated the correct diagnosis and therefore the correct treatment of cardiac patients. Definition Ebstein's anomaly is a rare congenital disorder, present at birth, in which the tricuspid valve is malformed and the valve itself is not in the correct anatomical location (Mayo Clinic Staff). This abnormality affects the right side of the heart: the tricuspid valve is located too deep in the ventricle, resulting in a smaller and weaker right ventricle. The space above the diminished right ventricle is made up of atrial tissue and this may be called right ventricular dysplasia or atrialized right ventricle (Reynolds). Typically, the tricuspid valve has three freely moving leaflets, but in Ebstein's anomaly, one or two of these leaflets fuse with the heart walls, causing regurgitation. Since the heart does not work as efficiently in those with this abnormality, the heart usually compensates and enlarges. This is......middle of document......at http://www.ebsteinsanomaly.org/what_is_ea.htmlHartnell, G. (July 22, 2013). Imaging of Ebstein anomalies. Accessed January 23, 2014, from http://emedicine.medscape.com/article/349278-overview#a24Mayo Clinic Staff (nd). Causes of Ebstein's Anomaly - Diseases and Conditions - Mayo Clinic. Accessed January 23, 2014, from http://www.mayoclinic.org/diseases-conditions/ebsteins-anomaly/basics/causes/con-20033605 Riaz, K. (2013, April 15). Ebstein anomaly. Retrieved January 23, 2014, from http://emedicine.medscape.com/article/154447-overview#a0101Swiss Medical Weekly (2005). Ebstein's anomaly – examination of a multifaceted congenital heart disease. Accessed February 22, 2014 at http://www.smw.ch/docs/pdf200x/2005/19/smw-10985.PDFTidy, C. (December 10, 2012). Ebstein's anomaly. Accessed February 22, 2014 from http://www.patient.co.uk/doctor/ebsteins-anomaly